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KMID : 1144020170130010047
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Journal of Korean Association for Disability and Oral Health
2017 Volume.13 No. 1 p.47 ~ p.51
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DENTAL TREATMENT OF A PATIENT WITH HADDAD SYNDROME UNDER GENERAL ANESTHESIA - CASE REPORT -
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Suh Hee-Won
Song Ji-Soo
Shin Teo-Jeon
Hyun Hong-Keun
Kim Young-Jae
Kim Jung-Wook
Lee Sang-Hoon
Jang Ki-Taeg
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Abstract
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Haddad syndrome, the association of Congenital Central Hypoventilation Syndrome (CCHS) and Hirschsprung’s disease (HD), is a disease caused by mutation of PHOX2B gene. This disease, which occurs very rarely worldwide, is characterized by adequate ventilation during wakefulness and hypoventilation during sleep due to decreased ventilatory sensitivity. In this case report, we report a case of dental treatment under general anesthesia in a child with Haddad syndrome.
A 3-year-old child with Haddad syndrome visited Seoul National University Dental Hospital for dental treatment. Dental treatment was planned under general anesthesia because of his medical condition. Treatment was successfully done without any postoperative complications. This case suggests that general anesthesia may be advantageous for dental treatment due to the risk of respiratory depression in a child with Haddad syndrome.
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KEYWORD
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Haddad syndrome, Congenital Central hypoventilation syndrome, Hirschsprung’s disease, Dental treatment, General anesthesia
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